Basal encephalocele associated with morning glory syndrome: case report

Basal encephalocele associated with morning glory syndrome: case report

Alternative title Encefalocele basal associada a síndrome morning glory: relato de caso
Author Minotto, Ivanete Autor UNIFESP Google Scholar
Abdala, Nitamar Autor UNIFESP Google Scholar
Miachon, Adriana Aparecida Siviero Autor UNIFESP Google Scholar
Spinola-Castro, Angela Maria Autor UNIFESP Google Scholar
Imamura, Paulo Autor UNIFESP Google Scholar
Nogueira, Roberto Gomes Autor UNIFESP Google Scholar
Institution Universidade Federal de São Paulo (UNIFESP)
Abstract The basal encephaloceles refer to rare entities and they correspond to herniation of brain tissue through defects of skull along the cribiform plate or the sphenoid bone. A rare morning glory syndrome, with characteristic retinal defect has been reported in association with basal encephaloceles. Hypophysis hormonal deficiencies may occur. We accounted for a pituitary dwarfism with delayed diagnosed transsphenoidal encephalocele associated with morning glory syndrome, showing the alterations found in retinography, computed tomography and magnetic resonance imaging.

As encefaloceles basais são entidades raras e correspondem a herniações do tecido cerebral através de um defeito do crânio, ao longo da lâmina crivosa etmoidal ou do osso esfenoidal. A rara síndrome morning glory, com alterações de fundo de olho características pode apresentar-se associada à encefalocele basal. Deficiências hormonais hipofisárias podem ocorrer. Relatamos caso de nanismo hipofisário com encefalocele transesfenoidal de diagnóstico tardio associada à síndrome de morning glory, mostrando as alterações na retinografia, tomografia computadorizada e ressonância magnética.
Keywords basal encephalocele
morning glory syndrome
computed tomography
magnetic resonance imaging
pituitary dwarfism
encefalocele basal
síndrome de morning glory
tomografia computadorizada
ressonância magnética
nanismo hipofisário
Language English
Date 2007-12-01
Published in Arquivos de Neuro-Psiquiatria. Academia Brasileira de Neurologia - ABNEURO, v. 65, n. 4a, p. 988-991, 2007.
ISSN 0004-282X (Sherpa/Romeo)
Publisher Academia Brasileira de Neurologia - ABNEURO
Extent 988-991
Origin http://dx.doi.org/10.1590/S0004-282X2007000600013
Access rights Open access Open Access
Type Article
SciELO ID S0004-282X2007000600013 (statistics in SciELO)
URI http://repositorio.unifesp.br/handle/11600/4052

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