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Author Coeli, Flavia Regina Autor UNIFESP Google Scholar
Maced, Danielle Mazziero Autor UNIFESP Google Scholar
Batista, Mariana Dias Autor UNIFESP Google Scholar
Pereira Cestari, Silmara da Costa Autor UNIFESP Google Scholar
Rotta, Osmar Autor UNIFESP Google Scholar
Institution Universidade Federal de São Paulo (UNIFESP)
Abstract Papillon-Lefevre syndrome, or palmoplantar keratoderma with periodontitis, is a rare genodermatosis with cutaneous and dental repercussions. the condition appears at around the first year of life, with transgressive palmar-plantar keratoderma associated with periodontitis, early loss of both deciduous and permanent teeth. It is frequently associated with pyogenic infection of the skin and internal organs. Histopathology is nonspecific, the diagnosis being eminently clinical.
Keywords Dipeptidyl peptidase I
Language Portuguese
Date 2008-07-01
Published in Anais Brasileiros de Dermatologia. Rio de Janeiro Rj: Soc Brasileira Dermatologia, v. 83, n. 4, p. 375-377, 2008.
ISSN 0365-0596 (Sherpa/Romeo, impact factor)
Publisher Soc Brasileira Dermatologia
Extent 375-377
Access rights Open access Open Access
Type Editorial
Web of Science ID WOS:000259968300015
SciELO ID S0365-05962008000400015 (statistics in SciELO)

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